December 6th Conference Pearls

Pediatric Abdominal Trauma (Dr. Blumberg):

  • Number one initially UNrecognized causes of death in pediatrics
  • Relatively larger organs compared to body sizes –> increase in injury
  • Children can maintain BP even up to 30% blood volume loss so hypotension is a late sign of hemorrhage
  • Less likely to scan children 2/2 concern for radiation in children
  • PECARN Abdomen variables:
    • Evidence of abdominal wall trauma or seat-belt sign
    • GCS < 14
    • Abdominal tenderness
    • Evidence of thoracic wall trauma
    • Complaints of abdominal pain
    • Decreased breath sounds
    • Vomiting
  • These 7 variables identified 197 out of the 203 patients with intraabdominal injuries
  • Of the 5034 patients deemed very low risk (no prediction variables present), 6 had intraabdominal injuries, requiring interventions
  • Data: Sensitivity 97%, Specific 43%, Negative PPV near 100%, Positive PPV 3%, negative LR 0.07

Pediatric SIM Case (Hemolytic Uremic Syndrome):

  • Ask parents about bloody diarrhea
  • HUS Classification
    • Diarrhea (typical) VS no-diarrhea (atypical)
    • Primary VS Secondary
      • Primary: defects in complement activation system
      • Secondary causes: infection (E. Coli, S. PNA, HIV), drug toxicity, autoimmune
    • Classic Triad (after prodromal period of diarrhea)
      • Microangiopathic hemolytic anemia
        • Hb < 8 g/dL
        • Peripheral blood smear: large number of schistocytes and helmet cells
        • Negative Coomb’s test
      • Thrombocytopenia
        • Platelets usually ~40,000/mm3
      • Acute kidney injury
        • Can range from hematuria to proteinuria to elevated BUN/Cr
        • Decreased urine output
    • How can I differentiate HUS from DIC?
      • DIC can reveal:
        • Prolonged PT and PTT
        • Elevated levels of fibrin degradation products and D-Dimer
    • MCC of HUS = Shiga-toxin producing E. Coli (EHEC 0157:H7)
    • Management:
      • Monitor fluid status carefully
        • Usually dehydrated and require bolus (20cc/kg)
        • Sometimes, oliguric or anuric patients may be fluid overloaded
        • May require dialysis, depending on degree of renal failure and complications
      • Transfuse for hemoglobin <6 g/dL for goal of 8-9 g/dL
      • Rarely have to transfuse platelets (only if active bleeding or <30,000/mm3 and requiring invasive procedure)
      • Monitor for seizures
      • Avoid antibiotics (unless sepsis is strongly suspected) because of potential release of Shiga toxin from lysis of bacterial cells
      • As discussed by Carlo and Dr. Restivo, final common pathway between HUS and TTP is ADAMTS-13 depletion. Therefore, can consider plasma exchange with FFP to remove the autoantibodies to ADAMTS13 protein and replete it
    • For further reading, check out EMDocs post

Adult SIM Case (Tumor Lysis Syndrome)

  • Massive tumor cell breakdown –> release of large amounts of potassium, phosphate and nucleic acids
    • Catabolism of nucleic acids to uric acid –> hyperuricemia –> precipitation of uric acid in renal tubules –> AKI
    • Hyperphosphatemia with calcium phosphate deposition in renal tubules –> AKI
    • Hyperkalemia –> cardiac arrest
  • Laboratory Criteria (from UpToDate)
    • Uric Acid > 8 mg/dL
    • Potassium > 6 mEq/L
    • Phosphorous >4.5 mg/dL
    • Calcium < 7 mg/dL
  • Clinical tumor lysis syndrome = laboratory criteria + at least 1 clinical complication
  • Most often occurs after initiation of cytotoxic therapy in aggressive lymphomas and T-cell ALL
  • Can also occur spontaneously prior to onset of chemo (especially in non-Hodgkin lymphoma)
  • Management:
    • Treat electrolyte abnormalities
    • Can use Rasburicase at 0.2mg/kg (if not given initially as prophylaxis)
    • Fluids (to wash out obstructing uric acid crystals)
    • Should be admitted to ICU
    • Consider renal consult for possible dialysis
  • If initial calcium dose for hyperkalemia is not effective (ex: persistently bradycardia), repeat dose!

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